The solid pseudopapillary tumor of the pancreas (SPT), also known as a Frantz tumor, was first identified in 1959 by its namesake. This uncommon pancreatic tumor, previously known as papillary epithelial neoplasm, low-grade papillary neoplasm, or solid and papillary neoplasm, predominantly affects younger individuals, with a notable female predominance. Its cellular origin remains uncertain, with potential links to acinar, endocrine, ductal, or progenitor cells. Characterized by a favorable prognosis and low malignant potential, it constitutes under 3% of exocrine pancreatic tumors. While most SPTs are benign, malignancy occurs in up to 15% of cases. This report describes an unusual case of a 19-year-old female who presented with epigastric pain, was treated with surgical resection, and was confirmed as a Frantz tumor via histopathology and immunohistochemistry.
